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METHACRYLYL COA

  • Methacrylyl-CoA
  • Chemical compound

    Methacrylyl-CoA is an intermediate in the metabolism of valine. v t e

    Methacrylyl-CoA

    Methacrylyl-CoA

  • Methylcrotonyl-CoA
  • Chemical compound

    3-Methylcrotonyl-CoA (β-Methylcrotonyl-CoA or MC-CoA) is an intermediate in the metabolism of leucine. It is found in mitochondria, where it is formed

    Methylcrotonyl-CoA

    Methylcrotonyl-CoA

    Methylcrotonyl-CoA

  • HMG-CoA
  • Chemical compound

    β-methylglutaconyl-CoA (MG-CoA) and β-hydroxy β-methylbutyryl-CoA (HMB-CoA). HMG-CoA reductase catalyzes the conversion of HMG-CoA to mevalonic acid,

    HMG-CoA

    HMG-CoA

    HMG-CoA

  • Crotonyl-CoA
  • Chemical compound

    amino acids. Crotonyl-CoA is also involved in β-oxidation, where it is formed from butyryl-CoA through the action of acyl-CoA dehydrogenases, linking

    Crotonyl-CoA

    Crotonyl-CoA

    Crotonyl-CoA

  • 3-Methylglutaconyl-CoA
  • Chemical compound

    3-Methylglutaconyl-CoA (MG-CoA), also known as β-methylglutaconyl-CoA, is an intermediate in the metabolism of leucine. It is metabolized into HMG-CoA. Methylcrotonyl-CoA

    3-Methylglutaconyl-CoA

    3-Methylglutaconyl-CoA

    3-Methylglutaconyl-CoA

  • Acetyl-CoA
  • Chemical compound

    ]] [[ ]] [[ ]] [[ ]] [[ ]] [[ ]] [[ ]] [[ ]] [[ ]] [[ ]] [[ ]] ]] Acetyl-CoA (acetyl coenzyme A) is a molecule that participates in many biochemical reactions

    Acetyl-CoA

    Acetyl-CoA

    Acetyl-CoA

  • Acetoacetyl-CoA
  • Chemical compound

    Acetoacetyl CoA is the precursor of HMG-CoA in the mevalonate pathway, which is essential for cholesterol biosynthesis. It also takes a similar role in

    Acetoacetyl-CoA

    Acetoacetyl-CoA

    Acetoacetyl-CoA

  • Leucine
  • Chemical compound

    isovaleryl-CoA. Isovaleryl-CoA is subsequently metabolized by isovaleryl-CoA dehydrogenase and converted to MC-CoA, which is used in the synthesis of acetyl-CoA

    Leucine

    Leucine

    Leucine

  • Β-Hydroxy β-methylbutyryl-CoA
  • Chemical compound

    β-Hydroxy β-methylbutyryl-coenzyme A (HMB-CoA), also known as 3-hydroxyisovaleryl-CoA, is a metabolite of L-leucine that is produced in the human body

    Β-Hydroxy β-methylbutyryl-CoA

    Β-Hydroxy β-methylbutyryl-CoA

    Β-Hydroxy_β-methylbutyryl-CoA

  • Methylmalonyl-CoA
  • Chemical compound

    the citric acid cycle. Methylmalonyl-CoA can be synthesized in two ways: From propionyl-CoA: Methylmalonyl-CoA results from the metabolism of fatty acid

    Methylmalonyl-CoA

    Methylmalonyl-CoA

    Methylmalonyl-CoA

  • Succinyl-CoA
  • Chemical compound

    Succinyl-coenzyme A, abbreviated as succinyl-CoA (/ˌsʌksɪnəlˌkoʊˈeɪ/) or SucCoA, is a thioester of succinic acid and coenzyme A. It is an important intermediate

    Succinyl-CoA

    Succinyl-CoA

  • Propionyl-CoA
  • Chemical compound

    yield both propionyl-CoA as well as acetyl-CoA. Propionyl-CoA is later converted into succinyl-CoA through biotin-dependant propionyl-CoA carboxylase (PCC)

    Propionyl-CoA

    Propionyl-CoA

  • Isobutyryl-CoA
  • Chemical compound

    produces isobutyryl-CoA from α-ketoisovaleric acid. α-Ketoisovaleric acid + CoA + NAD+       CO2 + H+   CO2 + H+   Isobutyryl-CoA + NADH   The substrates

    Isobutyryl-CoA

    Isobutyryl-CoA

  • Cysteine
  • Proteinogenic amino acid

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Cysteine

    Cysteine

    Cysteine

  • Isoleucine
  • Chemical compound

    skeleton is oxidised and split into propionyl-CoA and acetyl-CoA. Propionyl-CoA is converted into succinyl-CoA, a TCA cycle intermediate which can be converted

    Isoleucine

    Isoleucine

    Isoleucine

  • Lysine
  • Amino acid

    between acetyl-CoA and α‑ketoglutarate catalysed by homocitrate-synthase (HCS) (E.C 2.3.3.14) to give the intermediate homocitryl‑CoA, which is hydrolysed

    Lysine

    Lysine

    Lysine

  • Glutathione
  • Ubiquitous antioxidant compound in living organisms

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Glutathione

    Glutathione

    Glutathione

  • Methionine
  • Sulfur-containing amino acid

    for acetyl-CoA and succinyl-CoA is dictated by a single residue. The physiological basis for the preference of acetyl-CoA or succinyl-CoA is unknown,

    Methionine

    Methionine

    Methionine

  • 2-Methylbutyryl-CoA
  • Chemical compound

    2-Methylbutyryl-CoA is an intermediate in the metabolism of isoleucine. 2-Methylbutyryl-CoA dehydrogenase deficiency Ensenauer (23 April 2002). "Clinical

    2-Methylbutyryl-CoA

    2-Methylbutyryl-CoA

  • Creatinine
  • Breakdown product of creatine phosphate

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Creatinine

    Creatinine

    Creatinine

  • Cadaverine
  • Foul-smelling diamine compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Cadaverine

    Cadaverine

    Cadaverine

  • 3-Hydroxyisobutyryl-CoA
  • Chemical compound

    3-Hydroxyisobutyryl-CoA (or 3-hydroxy-2-methylpropanoyl-CoA) is an intermediate in the metabolism of valine. 3-hydroxyisobutyryl-CoA hydrolase 3-Hydroxyisobutyryl-CoA deacylase

    3-Hydroxyisobutyryl-CoA

    3-Hydroxyisobutyryl-CoA

  • Threonine
  • Amino acid

    dehydrogenase. An intermediate in this pathway can undergo thiolysis with CoA to produce acetyl-CoA and glycine. In humans the gene for threonine dehydrogenase is

    Threonine

    Threonine

    Threonine

  • Citrulline
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Citrulline

    Citrulline

    Citrulline

  • Pyruvic acid
  • Simplest of the alpha-keto acids

    gluconeogenesis, or converted to fatty acids through a reaction via acetyl-CoA. It can also be used to construct the amino acid alanine and can be converted

    Pyruvic acid

    Pyruvic_acid

  • Glutaryl-CoA
  • Chemical compound

    glutaryl-CoA dehydrogenase causes glutaric acidemia type 1, an autosomal recessive metabolic disorder.In this disorder, impaired metabolism of glutaryl-CoA is

    Glutaryl-CoA

    Glutaryl-CoA

    Glutaryl-CoA

  • Alanine
  • Α-amino acid that is used in the biosynthesis of proteins

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Alanine

    Alanine

    Alanine

  • Α-Ketobutyric acid
  • Chemical compound

    propionyl-CoA carboxylase with biotin as a cofactor to produce (S)-methylmalonyl-CoA. This is subsequently converted to (R)-methylmalonyl-CoA by mitochondrial

    Α-Ketobutyric acid

    Α-Ketobutyric acid

    Α-Ketobutyric_acid

  • Fumaric acid
  • Organic compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Fumaric acid

    Fumaric acid

    Fumaric_acid

  • Histidine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Histidine

    Histidine

    Histidine

  • Putrescine
  • Foul-smelling organic chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Putrescine

    Putrescine

    Putrescine

  • Arginine
  • Amino acid

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Arginine

    Arginine

    Arginine

  • Oxaloacetic acid
  • Organic compound

    acetyl-CoA. In previous stages acetyl-CoA is transferred from the mitochondria to the cytoplasm where fatty acid synthase resides. The acetyl-CoA is transported

    Oxaloacetic acid

    Oxaloacetic acid

    Oxaloacetic_acid

  • Serine
  • Amino acid

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Serine

    Serine

    Serine

  • Tiglyl-CoA
  • Chemical compound

    Tiglyl-CoA is an intermediate in the metabolism of isoleucine. It is an inhibitor of N-acetylglutamate synthetase. ROBINSON WG; BACHHAWAT BK; COON MJ

    Tiglyl-CoA

    Tiglyl-CoA

  • Β-Hydroxy β-methylbutyric acid
  • Chemical compound

    β-methylbutyryl-CoA (HMB-CoA). HMB-CoA is metabolized by either enoyl-CoA hydratase or another uncharacterized enzyme, producing β-methylcrotonyl-CoA (MC-CoA) or

    Β-Hydroxy β-methylbutyric acid

    Β-Hydroxy β-methylbutyric acid

    Β-Hydroxy_β-methylbutyric_acid

  • Α-Ketoglutaric acid
  • Chemical compound

    citrate: citrate → cis-aconitate → isocitrate → α-ketoglutarate → succinyl-CoA → succinate → fumarate → malate → oxaloacetate → citrate In this cycle, the

    Α-Ketoglutaric acid

    Α-Ketoglutaric acid

    Α-Ketoglutaric_acid

  • Imidazole propionate
  • Pharmaceutical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Imidazole propionate

    Imidazole propionate

    Imidazole_propionate

  • Valine
  • Chemical compound

    isobutyryl-CoA through oxidative decarboxylation by the branched-chain α-ketoacid dehydrogenase complex. This is further oxidised and rearranged to succinyl-CoA

    Valine

    Valine

    Valine

  • Proline
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Proline

    Proline

    Proline

  • Agmatine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Agmatine

    Agmatine

  • S-Adenosyl methionine
  • Chemical compound found in all domains of life with largely unexplored effects

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    S-Adenosyl methionine

    S-Adenosyl methionine

    S-Adenosyl_methionine

  • Β-Leucine
  • Chemical compound

    subsequently metabolized into β-ketoisocaproate (β-KIC), β-ketoisocaproyl-CoA, and then acetyl-CoA by a series of uncharacterized enzymes. Kohlmeier M (May 2015)

    Β-Leucine

    Β-Leucine

    Β-Leucine

  • Ornithine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Ornithine

    Ornithine

    Ornithine

  • Β-Hydroxybutyryl-CoA
  • Chemical compound

    β-Hydroxybutyryl-CoA (or 3-hydroxybutyryl-coenzyme A) is an intermediate in the fermentation of butyric acid, and in the metabolism of lysine and tryptophan

    Β-Hydroxybutyryl-CoA

    Β-Hydroxybutyryl-CoA

    Β-Hydroxybutyryl-CoA

  • Glycine
  • Amino acid

    begins with the conversion of benzoate by butyrate-CoA ligase into an intermediate product, benzoyl-CoA, which is then metabolized by glycine N-acyltransferase

    Glycine

    Glycine

    Glycine

  • Homocysteine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Homocysteine

    Homocysteine

    Homocysteine

  • Glutaconyl-CoA
  • Chemical compound

    Glutaconyl-CoA is an intermediate in the metabolism of lysine. It is an organic compound containing a coenzyme substructure, which classifies it as a

    Glutaconyl-CoA

    Glutaconyl-CoA

  • Phosphocreatine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Phosphocreatine

    Phosphocreatine

    Phosphocreatine

  • C25H40N7O17P3S
  • Index of chemical compounds with the same molecular formula

    C25H40N7O17P3S (molar mass: 835.609 g/mol) may refer to: Crotonyl-CoA Methacrylyl-CoA This set index page lists chemical structure articles associated

    C25H40N7O17P3S

    C25H40N7O17P3S

  • N-Acetylputrescine
  • Endogenous GABA precursor

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    N-Acetylputrescine

    N-Acetylputrescine

    N-Acetylputrescine

  • 3-Hydroxyanthranilic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    3-Hydroxyanthranilic acid

    3-Hydroxyanthranilic acid

    3-Hydroxyanthranilic_acid

  • Phenylalanine
  • Type of α-amino acid

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Phenylalanine

    Phenylalanine

    Phenylalanine

  • Α-Ketoisocaproic acid
  • Chemical compound

    cofactors present, including cholesterol, acetyl-CoA, isovaleryl-CoA, and other biological molecules. Isovaleryl-CoA is the main compound synthesized from ɑ-KIC

    Α-Ketoisocaproic acid

    Α-Ketoisocaproic acid

    Α-Ketoisocaproic_acid

  • Cystathionine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Cystathionine

    Cystathionine

    Cystathionine

  • N-Acetyl-γ-aminobutyric acid
  • Endogenous GABA precursor

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    N-Acetyl-γ-aminobutyric acid

    N-Acetyl-γ-aminobutyric acid

    N-Acetyl-γ-aminobutyric_acid

  • Tyrosine
  • Amino acid

    ketone body, which is activated with succinyl-CoA, and thereafter it can be converted into acetyl-CoA, which in turn can be oxidized by the citric acid

    Tyrosine

    Tyrosine

    Tyrosine

  • Γ-L-Glutamyl-L-cysteine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Γ-L-Glutamyl-L-cysteine

    Γ-L-Glutamyl-L-cysteine

    Γ-L-Glutamyl-L-cysteine

  • Β-Ketoisocaproic acid
  • Chemical compound

    product in the leucine metabolic pathway are β-leucine and β-ketoisocaproyl-CoA, respectively. Kohlmeier M (May 2015). "Leucine". Nutrient Metabolism: Structures

    Β-Ketoisocaproic acid

    Β-Ketoisocaproic acid

    Β-Ketoisocaproic_acid

  • Tryptophan
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Tryptophan

    Tryptophan

    Tryptophan

  • 3-Hydroxyisobutyric acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    3-Hydroxyisobutyric acid

    3-Hydroxyisobutyric acid

    3-Hydroxyisobutyric_acid

  • Cis-Urocanic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Cis-Urocanic acid

    Cis-Urocanic acid

    Cis-Urocanic_acid

  • 3-Phosphoglyceric acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    3-Phosphoglyceric acid

    3-Phosphoglyceric acid

    3-Phosphoglyceric_acid

  • Kynurenine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Kynurenine

    Kynurenine

    Kynurenine

  • Glutamate-5-semialdehyde
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Glutamate-5-semialdehyde

    Glutamate-5-semialdehyde

    Glutamate-5-semialdehyde

  • N'-Formylkynurenine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    N'-Formylkynurenine

    N'-Formylkynurenine

    N'-Formylkynurenine

  • Allysine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Allysine

    Allysine

    Allysine

  • Anthranilic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Anthranilic acid

    Anthranilic acid

    Anthranilic_acid

  • Glutamic acid
  • Amino acid and neurotransmitter

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Glutamic acid

    Glutamic acid

    Glutamic_acid

  • 2-Methylacetoacetyl-CoA
  • Chemical compound

    2-Methylacetoacetyl-CoA is an intermediate in the metabolism of isoleucine. 3-hydroxy-2-methylbutyryl-CoA dehydrogenase v t e

    2-Methylacetoacetyl-CoA

    2-Methylacetoacetyl-CoA

  • Formiminoglutamic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Formiminoglutamic acid

    Formiminoglutamic acid

    Formiminoglutamic_acid

  • Cysteine sulfinic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Cysteine sulfinic acid

    Cysteine sulfinic acid

    Cysteine_sulfinic_acid

  • Glutamate-1-semialdehyde
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Glutamate-1-semialdehyde

    Glutamate-1-semialdehyde

    Glutamate-1-semialdehyde

  • 4-Maleylacetoacetic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    4-Maleylacetoacetic acid

    4-Maleylacetoacetic acid

    4-Maleylacetoacetic_acid

  • 1-Pyrroline-5-carboxylic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    1-Pyrroline-5-carboxylic acid

    1-Pyrroline-5-carboxylic acid

    1-Pyrroline-5-carboxylic_acid

  • Α-Ketoisovaleric acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Α-Ketoisovaleric acid

    Α-Ketoisovaleric acid

    Α-Ketoisovaleric_acid

  • Metabolic intermediate
  • Compounds in biochemical reactions

    Lipid intermediates: Fatty acid metabolism involves intermediates like acyl-CoA derivatives during β-oxidation or fatty acid synthesis. Nucleotide intermediates:

    Metabolic intermediate

    Metabolic_intermediate

  • Saccharopine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Saccharopine

    Saccharopine

    Saccharopine

  • Methylmalonic acid semialdehyde
  • Chemical compound

    which converts it to propionyl-CoA. Methylmalonic acid semialdehyde + CoA + NAD+       CO2 + H+   CO2 + H+   Propionyl-CoA + NADH   Voet, Donald (2011)

    Methylmalonic acid semialdehyde

    Methylmalonic acid semialdehyde

    Methylmalonic_acid_semialdehyde

  • S-Adenosyl-L-homocysteine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    S-Adenosyl-L-homocysteine

    S-Adenosyl-L-homocysteine

  • Glycocyamine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Glycocyamine

    Glycocyamine

    Glycocyamine

  • Urocanic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Urocanic acid

    Urocanic acid

    Urocanic_acid

  • 2-Aminomuconic semialdehyde
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    2-Aminomuconic semialdehyde

    2-Aminomuconic semialdehyde

    2-Aminomuconic_semialdehyde

  • Cysteine metabolism
  • γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Cysteine metabolism

    Cysteine_metabolism

  • 2-Oxoadipic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    2-Oxoadipic acid

    2-Oxoadipic acid

    2-Oxoadipic_acid

  • 4-Hydroxyphenylpyruvic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    4-Hydroxyphenylpyruvic acid

    4-Hydroxyphenylpyruvic acid

    4-Hydroxyphenylpyruvic_acid

  • 2,3-Dihydroxy-3-methylpentanoic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    2,3-Dihydroxy-3-methylpentanoic acid

    2,3-Dihydroxy-3-methylpentanoic acid

    2,3-Dihydroxy-3-methylpentanoic_acid

  • 3-Hydroxykynurenine
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    3-Hydroxykynurenine

    3-Hydroxykynurenine

    3-Hydroxykynurenine

  • Imidazol-4-one-5-propionic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Imidazol-4-one-5-propionic acid

    Imidazol-4-one-5-propionic acid

    Imidazol-4-one-5-propionic_acid

  • Homogentisic acid
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    Homogentisic acid

    Homogentisic acid

    Homogentisic_acid

  • L-Arginine L-pyroglutamate
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    L-Arginine L-pyroglutamate

    L-Arginine_L-pyroglutamate

  • 2-Amino-3-carboxymuconic semialdehyde
  • Chemical compound

    γ-Glutamylcysteine G→propionyl-CoA→ succinyl-CoA valine→ α-Ketoisovaleric acid Isobutyryl-CoA Methacrylyl-CoA 3-Hydroxyisobutyryl-CoA 3-Hydroxyisobutyric acid

    2-Amino-3-carboxymuconic semialdehyde

    2-Amino-3-carboxymuconic semialdehyde

    2-Amino-3-carboxymuconic_semialdehyde

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